periodontal manifestations and unusual radiographic features in a patient with sturge-weber syndrome: a case report

نویسندگان

mohammad taghi chitsazi

adileh shirmohammadi

nasrin rahmanpour

monir moradzadeh khiyavi

چکیده

the sturge-weber syndrome or encephalotrigeminal angiomatosis is a rare neurological and congenital disorder with a frequency of 1 in 50,000 births. this syndrome is a nonhereditary developmental condition and is characterized by the presence of congenital capillary malformation and a hamartomatous vascular proliferation involving the face (port-wine stain or facial birthmark), sometimes skull and the tissues of brain, jaws, oral soft and hard tissues and rarely other body organs. seizures, mental retardation, and cortical calcification (tram-tracks) and congenital glaucoma may be seen in this syndrome. we report here a 40-year-old female with sturge-weber syndrome associated with bilateral cutaneous capillary malformation on her face, neck, hands and feet and also gingival enlargement.

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عنوان ژورنال:
journal of periodontology and implant dentistry

جلد ۶، شماره ۱، صفحات ۲۸-۰

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